储存: -15°C to -25°C/1 year(Do not lower than -25°C)
克隆号: PT1095R
特异性: Endogenous
基因名称: SLC25A26,SAMC
蛋白名称: Mitochondrial S-adenosylmethionine carrier protein (SAM carrier) (Solute carrier family 25 member 26)
别名: SAMC
Organism-1: Human
基因ID-1: 115286
SwissProt-1: Q70HW3
Organism-2: Mouse
基因ID-2: 57279
SwissProt-2: Q9Z2Z6
背景: This gene product is one of several closely related mitochondrial-membrane carrier proteins that shuttle substrates between cytosol and the intramitochondrial matrix space. This protein mediates the transport of acylcarnitines into mitochondrial matrix for their oxidation by the mitochondrial fatty acid-oxidation pathway. Mutations in this gene are associated with carnitine-acylcarnitine translocase deficiency, which can cause a variety of pathological conditions such as hypoglycemia, cardiac arrest, hepatomegaly, hepatic dysfunction and muscle weakness, and is usually lethal in new born and infants. [provided by RefSeq, Jul 2008]
储存: -15°C to -25°C/1 year(Do not lower than -25°C)
克隆号: PT1095R
特异性: Endogenous
基因名称: SLC25A26,SAMC
蛋白名称: Mitochondrial S-adenosylmethionine carrier protein (SAM carrier) (Solute carrier family 25 member 26)
别名: SAMC
Organism-1: Human
基因ID-1: 115286
SwissProt-1: Q70HW3
Organism-2: Mouse
基因ID-2: 57279
SwissProt-2: Q9Z2Z6
背景: This gene product is one of several closely related mitochondrial-membrane carrier proteins that shuttle substrates between cytosol and the intramitochondrial matrix space. This protein mediates the transport of acylcarnitines into mitochondrial matrix for their oxidation by the mitochondrial fatty acid-oxidation pathway. Mutations in this gene are associated with carnitine-acylcarnitine translocase deficiency, which can cause a variety of pathological conditions such as hypoglycemia, cardiac arrest, hepatomegaly, hepatic dysfunction and muscle weakness, and is usually lethal in new born and infants. [provided by RefSeq, Jul 2008]