Peroxin 10 Polyclonal Antibody

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商品货号： PLA017571

适应性： 人,大鼠,小鼠,

￥600元

规格：

40μL 100μL 200μL

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MSDS

说明书

商品描述

基因名称： PEX10
蛋白名称： Peroxisome biogenesis factor 10
Human_gene_id： 5192
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=5192
Human_swiss_prot_no： O60683
Human_swiss_link： http://www.uniprot.org/uniprotkb/O60683/entry
Mouse_swiss_prot_no： B1AUE5
Mouse_swiss_link： http://www.uniprot.org/uniprot/B1AUE5
特异性： Peroxin 10 Polyclonal Antibody detects endogenous levels of Peroxin 10 protein.
组成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
来源： Polyclonal, Rabbit,IgG
稀释： WB 1:500 - 1:2000. IHC 1:100 - 1:300. ELISA: 1:40000.. IF 1:50-200
纯化工艺： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
浓度： 1 mg/ml
储存： -15°C to -25°C/1 year(Do not lower than -25°C)
说明书： 1
Msds： MSDS_Antibody.pdf
其他名称： PEX10; RNF69; Peroxisome biogenesis factor 10; Peroxin-10; Peroxisomal biogenesis factor 10; Peroxisome assembly protein 10; RING finger protein 69
实测条带： 45kD
功能： disease:Defects in PEX10 are a cause of adrenoleukodystrophy neonatal (NALD) [MIM:202370]. NALD is a peroxisome biogenesis disorder (PBD) characterized by the accumulation of very long-chain fatty acids, adrenal insufficiency and mental retardation.,disease:Defects in PEX10 are a cause of Zellweger syndrome (ZWS) [MIM:214100]. ZWS is a fatal peroxisome biogenesis disorder characterized by dysmorphic facial features, hepatomegaly, ocular abnormalities, renal cysts, hearing impairment, profound psychomotor retardation, severe hypotonia and neonatal seizures. Death occurs within the first year of life.,disease:Defects in PEX10 are the cause of peroxisome biogenesis disorder complementation group 7 (PBD-CG7) [MIM:602859]; also known as PBD-CGB. PBD refers to a group of peroxisomal disorders arising from a failure of protein import into the peroxisomal membrane or matrix. The PBD group is comprised of four disorders: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). ZWS, NALD and IRD are distinct from RCDP and constitute a clinical continuum of overlapping phenotypes known as the Zellweger spectrum. The PBD group is genetically heterogeneous with at least 14 distinct genetic groups as concluded from complementation studies.,function:Somewhat implicated in the biogenesis of peroxisomes.,similarity:Belongs to the pex2/pex10/pex12 family.,similarity:Contains 1 RING-type zinc finger.,subunit:Interacts with PEX19.,
相关产品： RS0001,RS0002,YM3028,YM3029
细胞定位： Peroxisome membrane ; Peripheral membrane protein .
组织表达： Brain,Lung,
科研货号： PLA017571

Peroxin 10 Polyclonal Antibody

Catalog No PLA017571

Product information

基因名称： PEX10
蛋白名称： Peroxisome biogenesis factor 10
Human_gene_id： 5192
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=5192
Human_swiss_prot_no： O60683
Human_swiss_link： http://www.uniprot.org/uniprotkb/O60683/entry
Mouse_swiss_prot_no： B1AUE5
Mouse_swiss_link： http://www.uniprot.org/uniprot/B1AUE5
特异性： Peroxin 10 Polyclonal Antibody detects endogenous levels of Peroxin 10 protein.
组成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
来源： Polyclonal, Rabbit,IgG
稀释： WB 1:500 - 1:2000. IHC 1:100 - 1:300. ELISA: 1:40000.. IF 1:50-200
纯化工艺： The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
浓度： 1 mg/ml
储存： -15°C to -25°C/1 year(Do not lower than -25°C)
说明书： 1
Msds： MSDS_Antibody.pdf
其他名称： PEX10; RNF69; Peroxisome biogenesis factor 10; Peroxin-10; Peroxisomal biogenesis factor 10; Peroxisome assembly protein 10; RING finger protein 69
实测条带： 45kD
功能： disease:Defects in PEX10 are a cause of adrenoleukodystrophy neonatal (NALD) [MIM:202370]. NALD is a peroxisome biogenesis disorder (PBD) characterized by the accumulation of very long-chain fatty acids, adrenal insufficiency and mental retardation.,disease:Defects in PEX10 are a cause of Zellweger syndrome (ZWS) [MIM:214100]. ZWS is a fatal peroxisome biogenesis disorder characterized by dysmorphic facial features, hepatomegaly, ocular abnormalities, renal cysts, hearing impairment, profound psychomotor retardation, severe hypotonia and neonatal seizures. Death occurs within the first year of life.,disease:Defects in PEX10 are the cause of peroxisome biogenesis disorder complementation group 7 (PBD-CG7) [MIM:602859]; also known as PBD-CGB. PBD refers to a group of peroxisomal disorders arising from a failure of protein import into the peroxisomal membrane or matrix. The PBD group is comprised of four disorders: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). ZWS, NALD and IRD are distinct from RCDP and constitute a clinical continuum of overlapping phenotypes known as the Zellweger spectrum. The PBD group is genetically heterogeneous with at least 14 distinct genetic groups as concluded from complementation studies.,function:Somewhat implicated in the biogenesis of peroxisomes.,similarity:Belongs to the pex2/pex10/pex12 family.,similarity:Contains 1 RING-type zinc finger.,subunit:Interacts with PEX19.,
相关产品： RS0001,RS0002,YM3028,YM3029
细胞定位： Peroxisome membrane ; Peripheral membrane protein .
组织表达： Brain,Lung,
科研货号： PLA017571

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